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New Avenues of Research in Fatty Acid Oxidation and Ketone Body Metabolism: the scientific legacy of Derek Williamson

Edited by
Simon Eaton & Patti A. Quant

The full text of this publication is available as a single pdf file or as separate files indicated by the links below.


1 Analysis of free and conjugated varanic acid diastereomers using HPLC electrospray tandem mass spectrometry in patients with D-bifunctional protein deficiency
Vreken P, Overmars H, van Lint L, Hunneman D.H., Wanders R.J.A.
Pages 1-4
2 Comparative effects of hemipalmitoylcarnitinium stereoisomers on hepatic mitochondrial carnitine palmitoyltransferases in the diabetic rat
Nicole E. Neptune, Prashant S. Savle, Isabella U. Nam, Richard D. Gandour, and Khosrow Kashfi
Pages 5-9
3 Fatty acid regulation of gene expression in adipogenesis and adipocyte metabolism
Eric Duplus, Martine Glorian and Claude Forest
Pages 11-16
4 Co-regulation of mitochondrial glycerol-3-phosphate acyltransferase and carnitine palmitoyltransferase I mRNA expression in carnitine- depleted rat liver and heart
P. Degrace, L. Demizieux, J. Gresti and P. Clouet
Pages 17-21
5 Shifted cooperation of desaturation and oxidation of palmitic acid in rat liver
L. Demizieux, P. Degrace, J. Gresti, M. Narce, J.-P. Poisson and P. Clouet
Pages 23-27
6 Co-ordination of oxidative and non-oxidative metabolism: a pivotal role for the pyruvate dehydrogenase kinases
Mary C. Sugden and Mark J. Holness
Pages 29-32
7 Mitochondrial carnitine/acylcarnitine translocase deficiency
L. IJlst, J.P.N. Ruiter, C.W.T. van Roermund and R.J.A. Wanders
Pages 33-37
8 D-3-Hydroxybutyrate dehydrogenase, a ketone body converting enzyme: regulation during the hibernation process
M. Kabine, M. Cherkaoui Malki, N. Latruffe and M.S. El Kebbaj
Pages 39-43
9 Fatty acid oxidation in Saccharomyces cerevisiae and the functional role of peroxisomal and cytosolic malate dehydrogenase in the re-oxidation of intraperoxisomal NADH
C.W.T. van Roermund and R.J.A. Wanders
Pages 45-50
10 2-Methyl branched-chain fatty acid -oxidation in peroxisomes and mitochondria and the role of 2-methylacyl-CoA racemase therein
S. Ferdinandusse, S. Denis, P. Vreken, H.R. Waterham and R.J.A. Wanders
Pages 51-57
11 2-Methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency, a new disorder of isoleucine and branched-chain fatty acid degradation: studies on the forward and reverse reactions
R.J.A. Wanders, J.P.N. Ruiter, S. Kuiper, J. Brand, M. Lindner, G. F. Hoffman, E. Mayatapek and J. Zschocke
Pages 59-61
12 Peroxisomes and PPARs : a key role in metabolism and cell differentiation
Joseph Vamecq, Louis Vallee and Norbert Latruffe
Pages 63-69

© retained by the authors of each chapter and permission to use or copy material should be sought directly from the corresponding author.

This Colloquium was held at the 672nd Biochemical Society Meeting at the University of Sussex in December 2000. The main speaker manuscripts are published in Biochemical Society Transactions, Volume 29, part 2, pp. 237-330. Biochemical Society Transactions is published by Portland Press, London, England, on behalf of the Biochemical Society. ISSN 0300-5127. Volume 29 part 2, 237-330

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